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KMID : 0358819780050010019
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Journal of Korean Society of Plastic and Reconstructive Surgeons
1978 Volume.5 No. 1 p.19 ~ p.23
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A Case of Diffuse Neurofibromatosis of the Head and Neck
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Abstract
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Diffuse neurofibromatosis or, von Recklinghausen´s disease is a hereditary, often congenital and sometimes familial disturbance in supportive tissue of the nervous system, both central and peripheral
It usually involves the skin. It may involve the skeleton and disturbances in other systems such as the endocrine and gastro-intestinal tract have reported.
The authors experienced a case of neurofibromatosis of the head and neck.
The patient was 21 year-old male. Examination of the left temporal and cheek showed light brown patch and soft painless pedunculated nodule formed hanging mass. Also cafe-au-lait spots and freckling showed on the back, anterior chest wall and both axillary vaults. Moderate ptosis was noted at the left eyelid because of the hanging mass.
Histologically, the preparation showed whorls of spindle cells in fibrous tissue with wavy or interlacing fashion and melanin deposition in the basal cell layer of the skin.
It was treated by the use of local tissue flap after subtotal excision of the mass.
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KEYWORD
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